| Catalog No. | HY377316 |
| Brand | abinScience |
| Species reactivity | Human |
| Form | Liquid |
| Storage buffer | 0.01M PBS pH 7.4 |
| Purity | >95% purity as determined by SDS-PAGE. |
| Clonality | Monoclonal |
| Isotype | A recombinant GAA/Aglucosidase alfa |
| Applications | ELISA, Functional assay, Research in vivo |
| Target | GAA, Lysosomal alpha-glucosidase, Acid maltase, Aglucosidase alfa |
| References | 1. Hermans MM, et al. Human lysosomal alpha-glucosidase: functional characterization of the glycosylation sites. The Biochemical journal. 1993 Feb 01;289 (Pt 3)(Pt 3):681-6. [HY377316] 2. Hoefsloot LH, et al. Primary structure and processing of lysosomal alpha-glucosidase; homology with the intestinal sucrase-isomaltase complex. The EMBO journal. 1988 Jun;7(6):1697-704. [HY377316] |
| Purification | Purified by Nickel column. |
| Biological activity | Lysosomal α-Glucosidase is a γ-amylase that is essential for the degradation of glycogen in lysosomes [1] [2]. |
| Endotoxin level | < 10 EU/mg |
| Expression system | Mammalian cells |
| Accession | P10253 |
| Stability and Storage | Use a manual defrost freezer and avoid repeated freeze thaw cycles. Store at 2 to 8°C for frequent use. Store at -20 to -80°C for twelve months from the date of receipt. |
| Note | For research use only. Not suitable for clinical or therapeutic use. |
Research Grade GAA/Aglucosidase Alfa
Overview
Images
 SDS-PAGE |
SDS-PAGE for Research Grade GAA/Aglucosidase Alfa |